RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58088841 T1 Uhl Anomaly T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58088841 RD 2024/03/29 AB A congenital disease characterized by the absence of a normal development of the myocardial layer of the right ventricle (usually replaced by fibrous or fatty tissue). Because the myocardial layer is dysplastic, the endocardium and epicardium are in apposition, which results in severe dilatation and early congestive cardiac failure. Chest radiography demonstrates marked cardiomegaly and right-sided chamber enlargement. Echocardiography and right-ventricle angiography demonstrate increased right heart volumes, severe diffuse hypokinesis, and tricuspid valve regurgitation.