RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58086447 T1 Sea-Blue Histiocytosis Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58086447 RD 2024/03/19 AB Genetic and acquired forms of this clinical entity exist. It is associated to the presence of sea-blue histiocytes in the bone marrow and a cholesterol ester storage disease. It is clinically characterized by the presence of splenomegaly, mild thrombocytopenia, and progressive neurological disease (e.g., ataxia, dementia and seizures).