RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58085370 T1 Riley-Smith Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58085370 RD 2024/03/28 AB A rare form of PTEN-MATCHS (phosphatase and tensin homologue-macrocephaly, autosomal dominant, thyroid disease, cancer, hamartomata, skin abnormalities) Syndrome. Close to Bannayan-Zonana Syndrome and characterized by macrocephaly, pseudopapilledema, hemangiomata, and multiple lipomas. Subcutaneous hemangioma may be present at birth or appear later in childhood. Multiple signs can be associated (head, chest, abdominal, and genital).