RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58083908 T1 Progressive Bulbar Palsy of Childhood T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58083908 RD 2024/03/19 AB A very rare inherited condition characterized by progressive degeneration of bulbar nuclei and anterior horn cells of the cranial nerves with little or no involvement of the spinal cord. Clinical features include significant atrophy of muscles innervated by cranial nerves and corticobulbar tracts, dysphagia, ptosis, bilateral facial weakness, absent gag reflex, and hyperreflexia.