RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58081327 T1 N-Acetylglutamate Synthetase Deficiency T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58081327 RD 2024/03/28 AB Congenital mitochondrial disorder of the metabolism of ammonium (hyperammonemia) leading to an anomaly in the urea cycle.