RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Marciniak, Bruno
A1 Dalens, Bernard J.
SR Print(0)
ID 58076114
T1 Microvillous Inclusion Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications
YR 2006
FD 2006
PB The McGraw-Hill Companies
PP New York, NY
SN 9780071354554
LK accessanesthesiology.mhmedical.com/content.aspx?aid=58076114
RD 2024/04/16
AB Extremely  rare  inherited  enteropathy  that  is  typically  apparent  within  hours  or  days  after  birth.  The  disorder  is  characterized  by  chronic,  severe,  watery  diarrhea  and  malabsorption  caused  by  hypoplasia  and/or  atrophy  of  the  wall  of  the  small  intestine  (e.g.,  hypoplastic  villus  atrophy,  defective  brush-border  assembly  and  differentiation).  In  infants,  chronic  diarrhea  and  malabsorption  may  result  in  severe  dehydration,  electrolyte  imbalance,  malnutrition,  failure  to  thrive,  and  acidosis.