RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58075505 T1 McCune-Albright Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58075505 RD 2024/03/29 AB Characterized by the triad of polyostotic fibrous dysplasia, café-au-lait skin pigmentation, and autonomous endocrine hyperfunction. The most common form of autonomous endocrine hyperfunction is gonadotropin-independent precocious puberty, but affected individuals also may have hyperthyroidism, hypercorticism, pituitary gigantism, or acromegaly. Nonendocrine abnormalities in this disorder include hypophosphatemia, chronic liver disease, tachycardia, and rarely sudden death, possibly from cardiac arrhythmias.