RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Marciniak, Bruno
A1 Dalens, Bernard J.
SR Print(0)
ID 58073873
T1 Leber Hereditary Optic Neuropathy (LHON)
T2 Syndromes: Rapid Recognition and Perioperative Implications
YR 2006
FD 2006
PB The McGraw-Hill Companies
PP New York, NY
SN 9780071354554
LK accessanesthesiology.mhmedical.com/content.aspx?aid=58073873
RD 2024/04/20
AB Rare  hereditary  form  of  optic  atrophy  that  usually  affects  young  males.  Characterized  by  sudden  bilateral  cloudiness  of  vision,  followed  by  scotoma,  rapid  deterioration  of  central  vision,  and  occasional  color  vision  disorders.  Associated  with  atrophy  of  the  optic  nerve  fibers  and  retinae.  Considered  a  mitochondrial  disease.  Cardiac  conduction  defects  have  been  reported  with  this  condition.