RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Marciniak, Bruno
A1 Dalens, Bernard J.
SR Print(0)
ID 58079076
T1 Hallervorden-Spatz Disease
T2 Syndromes: Rapid Recognition and Perioperative Implications
YR 2006
FD 2006
PB The McGraw-Hill Companies
PP New York, NY
SN 9780071354554
LK accessanesthesiology.mhmedical.com/content.aspx?aid=58079076
RD 2024/04/24
AB Inherited  disorder  characterized  by  progressive  degeneration  of  the  nervous  system  caused  by  iron  deposition  in  basal  ganglia.  Most  commonly  begins  in  childhood  as  a  dystonic  syndrome.  Other  clinical  features  include  distorting  muscle  contractions  of  the  face,  limbs,  and  trunk,  choreoathetosis,  muscle  rigidity,  spasticity,  seizures,  and  dementia.  Less  common  symptoms  include  painful  muscle  spasms,  mental  retardation,  and  visual  impairment.