RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58078006 T1 Glycogen Storage Disease Type I (GSD I) T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58078006 RD 2024/03/29 AB Severe inborn liver dysfunction caused by an almost total deficiency of hepatic glucose-6-phosphatase (type Ia) or a defect in intracellular transport of the enzyme substrate (type Ib), resulting in severe hypoglycemia and its consequences (seizures, cyanosis, apnea).