RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58071250 T1 Friedreich Ataxia (FRDA) T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58071250 RD 2024/03/29 AB Genetic disorder characterized by progressive dysfunction of the posterior spinal cord, cerebellum (ataxia, nystagmus), and peripheral nerves. It typically becomes apparent before adolescence. Clinical features include unsteady posture, frequent falling, progressive ataxia, characteristic foot deformities, increasing incoordination of the arms and hands, dysarthria, and nystagmus. It may be associated with cardiomyopathy, chest pain, arrhythmias, and diabetes mellitus. All patients have normal intelligence.