RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Marciniak, Bruno
A1 Dalens, Bernard J.
SR Print(0)
ID 58069575
T1 Ectodermal Dysplasia
T2 Syndromes: Rapid Recognition and Perioperative Implications
YR 2006
FD 2006
PB The McGraw-Hill Companies
PP New York, NY
SN 9780071354554
LK accessanesthesiology.mhmedical.com/content.aspx?aid=58069575
RD 2024/04/24
AB Ectodermal  dysplasia  is  a  rare  group  of  inherited  disorders.  It  was  first  described  by  Charles  Darwin  in  1875.  The  disorders  arise  from  disturbances  in  one  or  more  ectodermal  structures  and  their  accessory  appendages.  The  absence,  or  deficient  function,  of  at  least  two  derivatives  of  the  ectoderm  constitutes  a  form  of  ectodermal  dysplasia.  Each  combination  of  defects  represents  another  type  of  ectodermal  dysplasia  and  has  a  specific  name.  At  least  150  different  forms  of  ectodermal  dysplasia  have  been  identified;  some  of  the  most  common  are  presented  here.