RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Marciniak, Bruno A1 Dalens, Bernard J. SR Print(0) ID 58067357 T1 Congenital Pancreatic Agenesis T2 Syndromes: Rapid Recognition and Perioperative Implications YR 2006 FD 2006 PB The McGraw-Hill Companies PP New York, NY SN 9780071354554 LK accessanesthesiology.mhmedical.com/content.aspx?aid=58067357 RD 2023/03/27 AB This extremely rare condition results in early-onset insulin-dependent diabetes mellitus (IDDM) and exocrine pancreatic insufficiency.