RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164087628 T1 Von Gierke Disease T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164087628 RD 2024/03/29 AB An inborn error of glycogen metabolism caused by glucose-6-phosphatase (G6P) deficiency. The disease is characterized by hepatomegaly, hypoglycemia, and hyperlacticacidemia. Lethal in infancy or childhood if untreated.