RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164087074 T1 Uhl Anomaly T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164087074 RD 2024/04/19 AB An extremely rare congenital heart defect characterized by a near total absence of the myocardium of the parietal wall of the right ventricle resulting in severe dilatation and early congestive cardiac failure. Increased right heart volumes, severe diffuse hypokinesis, and tricuspid valve regurgitation. Fatal without intervention.