RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164085169 T1 Sialidosis T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164085169 RD 2023/03/24 AB Agenetic neurodegenerative disease (oligosaccharidosis) caused by a deficiency in α-N-acetyl neuraminidase (or sialidase) leading to excessive tissue sialyloligosaccharides (sialylated oligosaccharides) in nerve cells.