RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164083512
T1 Reticular Dysgenesia
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164083512
RD 2024/04/19
AB One  of  the  rarest  and  most  severe  forms  of  ☞Severe  Combined  Immunodeficiency  Syndrome  (SCIDS)  characterized  by  sensorineural  deafness,  agranulocytosis,  lymphopenia,  and  lymphoid  and  thymic  hypoplasia  with  absent  cellular  and  humoral  immunity  functions.  Prognosis  is  generally  poor  in  the  first  weeks  of  life.