RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164079812 T1 Myopathy, Distal, Welander Type T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164079812 RD 2024/03/28 AB It is a genetic disorder characterized by distal, late-onset myopathy. The presenting feature is in 89% of cases weakness and wasting of the small long extensor muscles of the hands and feet. Myotonia and sensory changes are not present. It gradually affects the distal muscles of the lower extremities. The association between this disorder and heart problems is not as frequent as it is the case with congenital myopathies. However, cardiomyopathic cases have been reported.