RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164078396
T1 Meretoja Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164078396
RD 2024/04/19
AB It  is  a  primary  hereditary  systemic  amyloidosis  (Type  II)  characterized  by  cardiac  and  airway  implications.  Clinical  features  include  corneal  lattice  dystrophy  and  cranial  neuropathy  (eg,  facial  paresis),  nephrotic  syndrome  and  renal  failure,  and  cutis  laxa.  Progressive  peripheral  polyneuropathy  is  mainly  affecting  vibration  and  touch  senses  is  a  feature  present  in  these  individuals.  The  onset  of  the  disease  begins  much  later  in  life  usually  around  the  age  of  50  to  70  years.