RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164078324 T1 Melnick-Needles Syndrome (MNS) T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164078324 RD 2024/03/29 AB It is a genetic disorder characterized by abnormal bone development. Bowing of the bones in the arms and legs is characteristic. Particular facial appearance includes hypertelorism, full cheeks, small facial bones, and severe micrognathia. Other clinical features include a relatively small chest cavity with irregular ribbon-like ribs, short clavicle, short stature, and narrow shoulders. Pectus excavatum is often present. Occasionally, dislocation of the hip occurs. May present hydronephrosis caused by urinary retention caused by small ureters. There is some suggestion that the entity is a form of the fronto-otopalatodigital osteodysplasia syndrome.