RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164076276 T1 Landouzy-Dejerine Dystrophy T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164076276 RD 2024/10/08 AB It is a genetically transmitted neuromuscular disease with a slow progression and characterized by weakness of facial, shoulder, and/or upper arm muscles. Nowadays it is more frequently called Facio-Scapulo-Humeral Muscular Dystrophy. It is characterized by muscle weakness and atrophy in the upper body. The presence of muscle atrophy in the hamstring and trunk muscles is more frequent than reported. The disease is clinically present before the age of 20 years. The onset may be as early as infancy or rarely later in adulthood. Life expectancy is not shortened.