RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164074760
T1 Kartagener Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164074760
RD 2024/04/25
AB It  is  genetically  transmitted  autosomal  dominant  disease  normally  called  “Primary  Ciliary  Dyskinesia”  when  it  only  includes  the  ciliopathic  disease.  It  is  characterized  by  chronic  recurrent  respiratory  infections,  sinusitis,  bronchitis,  pneumonia,  and  otitis  media.  However,  in  the  presence  of  bronchiectasis,  situs  inversus,  and  chronic  sinusitis,  it  is  known  as  Kartagener  Syndrome.  The  situs  inversus  is  present  only  in  50%  of  primary  ciliary  dyskinesia  cases.