RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164073815
T1 Incontinentia Pigmenti
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164073815
RD 2024/04/25
AB It  is  a  genetic  disease  characterized  by  unusual  patterns  of  discolored  skin.  During  the  first  stage,  skin  redness  and  spiral  lines  of  blisters  are  encountered.  Second  stage  includes  warty  skin  on  the  arms  and  legs.  Third  stage  is  associated  with  discolorations  of  the  skin  but  also  hair  (kinky  hairs)  and  teeth.  Other  features  include  central  nervous  system  dysfunction  (spina  bifida,  skull  deformity),  dwarfism,  clubfeet,  cleft  palate/lip,  syndactyly,  retinal  vascular  abnormalities,  blindness,  and  congenital  dislocation  of  the  hips.