RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164073246 T1 Hurler Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164073246 RD 2024/03/28 AB Genetically transmitted lysosomal storage disease resulting in accumulation of acid mucopolysaccharides in the central nervous system and peripheral tissues characterized by coarse facies (gargoyle-like), profound mental retardation, considerable hepatomegaly, hernias, enlarged tongue, skeletal disorders (kyphoscoliosis), dwarfism, and respiratory and cardiac impairment.