RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164072553
T1 Hereditary Hemorrhagic Telangiectasia
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164072553
RD 2024/04/23
AB Autosomal  dominant  mucocutaneous  and  visceral  fibrovascular  dysplasia  in  which  telangiectasia,  arteriovenous  malformations,  and  vascular  aneurysms  may  be  widely  distributed  throughout  the  cardiovascular  system.  It  is  usually  recognized  as  a  “triad”  of  telangiectasia,  recurrent  epistaxis,  and  a  family  history  of  the  disorder.  The  telangiectasias  are  located  on  the  skin  and  mucosa  of  the  nose  and  gastrointestinal  tract.  Epistaxis  is  the  most  common  problem.  The  presence  of  arteriovenous  malformations  is  predominant  in  the  lungs  (50%),  liver  (30-70%),  and  the  brain  (10%),  with  a  very  small  proportion  (<1%)  in  the  spinal  cord.