RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164071456 T1 Gorlin-Goltz Syndrome T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164071456 RD 2024/03/29 AB Autosomal dominant inherited ectodermal disorder characterized by basal cell nevi on the torso and shoulders with a potential of malignant degeneration. Gorlin-Goltz Syndrome is an autosomal dominant inherited disorder characterized by the presence of multiple odontogenic keratocysts along with various cutaneous, dental, osseous, ophthalmic, neurological, and sex organ abnormalities. Early diagnosis is essential as it may progress to aggressive basal cell carcinomas and neoplasias. Multiple cysts of variable size can be found in the maxilla, mandible and airway, and may make endotracheal intubation difficult.