RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164070625
T1 Generalized Arterial Calcification of Infancy
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164070625
RD 2024/04/23
AB A  very  rare  metabolic  disorder  characterized  by  deposition  of  calcium  salts  in  the  internal  elastic  lamina  of  large-  and  medium-sized  arteries  causing  intimal  proliferation  and  leading  to  arterial  stenosis.  It  affects  the  aorta,  coronary  arteries,  iliac  vessels,  and  carotid  arteries.  Coronary  artery  disease  occurs  in  early  infancy  with  heart  failure  and  myocardial  infarction  within  the  first  months  of  life.  Although  survival  to  adulthood  has  been  reported,  death  usually  occurs  before  6  months  of  age.