RT Book, Section A1 Bissonnette, Bruno A1 Luginbuehl, Igor A1 Engelhardt, Thomas SR Print(0) ID 1164069732 T1 Fanconi Anemia T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e YR 2019 FD 2019 PB McGraw-Hill Education PP New York, NY SN 9781259861789 LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164069732 RD 2024/03/28 AB Fanconi anemia (FA) is the most frequently reported of the rare inherited bone marrow failure syndromes. It is a rare autosomal recessive inherited bone marrow failure syndrome with congenital and hematological abnormalities. Inherited anemia leading to bone marrow failure, myelogenous leukemia, and, in older patients, many cancers (head and neck, esophageal, gastrointestinal, vulvar, anal). It is recommended to use regional anesthesia when after confirming the absence of thrombocytopenia, in an attempt to limit the exposure to general anesthesia, particularly N2O. The presence of microcephaly (possible difficult tracheal intubation), hypothyroidism, and elevated liver enzymes must be evaluated before general anesthesia.