RT Book, Section
A1 Bissonnette, Bruno
A1 Luginbuehl, Igor
A1 Engelhardt, Thomas
SR Print(0)
ID 1164064209
T1 Camptodactyly-Arthropathy-Coxa Vara-Pericarditis (CACP) Syndrome
T2 Syndromes: Rapid Recognition and Perioperative Implications, 2e
YR 2019
FD 2019
PB McGraw-Hill Education
PP New York, NY
SN 9781259861789
LK accessanesthesiology.mhmedical.com/content.aspx?aid=1164064209
RD 2024/04/19
AB The  Camptodactyly-Arthropathy-Coxa  Vara-Pericarditis  Syndrome  is  a  rare  genetic  disorder  usually  present  at  birth  or  surely  noticed  within  the  first  year  of  life.  Arthropathy  typically  develops  between  3  and  8  years  of  age  and  is  resistant  to  anti-inflammatory  medications.  The  arthropathy  principally  involves  large  joints  such  as  elbows,  hips,  knees,  and  ankles.  Coxa  vara  occurs  in  50  to  90%  of  cases.  A  noninflammatory  constrictive  pericarditis  (30%)  may  be  present  in  the  first  or  second  decade  of  life  and  may  lead  to  pericardial  effusion.