TY - CHAP M1 - Book, Section TI - Von Gierke Disease A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Marciniak, Bruno A1 - Dalens, Bernard J. PY - 2006 T2 - Syndromes: Rapid Recognition and Perioperative Implications AB - An inborn error of glycogen metabolism caused by glucose-6-phosphatase (G6P) deficiency. The disease is characterized by hepatomegaly, hypoglycemia, and hyperlacticacidemia. Lethal in infancy or childhood. SN - PB - The McGraw-Hill Companies CY - New York, NY Y2 - 2024/04/16 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=58089348 ER -