TY  - CHAP
M1  - Book, Section
TI  - Gsell-Erdheim Syndrome
A1  - Bissonnette, Bruno
A1  - Luginbuehl, Igor
A1  - Marciniak, Bruno
A1  - Dalens, Bernard J.
PY  - 2006
T2  - Syndromes: Rapid Recognition and Perioperative Implications
AB  - Aneurysms  and  dissections  of  the  aorta  usually  result  from  degenerative  changes  in  the  aortic  wall.  Thoracic  aortic  aneurysms  and  dissections  are  primarily  associated  with  a  characteristic  histologic  appearance  known  as  “medial  necrosis”  or  “Erdheim  cystic  medial  necrosis”  which  is  characterized  by  degeneration  and  fragmentation  of  elastic  fibers,  loss  of  smooth  muscle  cells,  and  accumulation  of  basophilic  ground  substance.  The  association  between  congenital  bicuspid  aortic  valve  and  medial  necrosis  of  the  aorta  has  been  suggested.  Ectopia  of  the  pigment  layer  of  the  iris  onto  the  anterior  surface  of  the  iris  has  been  associated  with  this  medical  condition.  
SN  - 
PB  - The McGraw-Hill Companies
CY  - New York, NY
Y2  - 2024/04/23
UR  - accessanesthesiology.mhmedical.com/content.aspx?aid=58078718
ER  -