TY - CHAP M1 - Book, Section TI - Sialidosis A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - Agenetic neurodegenerative disease (oligosaccharidosis) caused by a deficiency in α-N-acetyl neuraminidase (or sialidase) leading to excessive tissue sialyloligosaccharides (sialylated oligosaccharides) in nerve cells. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164085169 ER -