TY - CHAP M1 - Book, Section TI - Maffucci Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a sporadic disorder characterized by an association of multiple enchondromas (benign tumors of cartilage), and cavernous hemangiomas are often involving the head and neck. The enchondromas affect the extremities and their distribution is asymmetrical. The most common sites of enchondromas are the metacarpal bones and phalanges of the hands. Lymphangiomas can also be present. Patients are normal at birth. The bone and cartilage deformities appear during childhood, usually between the ages of 1 to 5 years. However, it can also appear at puberty. Patients affected have pathologic fractures and sarcomas. There is a normal intelligence. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/15 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164077573 ER -