TY - CHAP M1 - Book, Section TI - Kenny-Caffey Syndrome (KCS) A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is an extremely rare hereditary skeletal dysplasia presenting clinically in two different forms. In general terms, the Kenny-Caffey Syndrome is characterized by proportionate dwarfism as a result of thickening of the inner corticalis and stenosis of the medullary cavities of the tubular bones. The signs of the disease are present at birth. Other features include short stature, hypocalcemia, hypoparathyroidism, and normal intelligence. The onset of hypocalcemia is usually present within infancy, the first 2 to 3 months of life, and is transient. It is established that hypocalcemia in adult may be due to stress or follow surgery or illness. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/28 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164075066 ER -