TY - CHAP M1 - Book, Section TI - Aicardi-Goutières Syndrome (AGS) A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - A rapidly progressive, familial encephalopathy with calcifications of the basal ganglia, cerebral white matter abnormalities, cerebral atrophy, progressive microcephaly, chronic cerebrospinal fluid (CSF) lymphocytosis, and elevated levels of interferon-α in CSF and serum. This syndrome may progress fast into a vegetative state and early death. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/04/24 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164061035 ER -