TY - CHAP M1 - Book, Section TI - Wohlfart-Kugelberg-Welander Syndrome A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Marciniak, Bruno A1 - Dalens, Bernard J. Y1 - 2006 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications AB - Juvenile spinal muscular atrophy, characterized by slowly progressive muscular weakness as a result of degeneration of anterior horn cells (spinal motor neurons). Onset is between the ages of 2 and 17 years. Early symptoms consist of atrophy and weakness of the proximal muscle of the extremities (mainly legs), followed by thoracic muscles. Should not be confused with muscular dystrophy syndromes. SN - PB - The McGraw-Hill Companies CY - New York, NY Y2 - 2024/03/28 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=58089980 ER -