TY  - CHAP
M1  - Book, Section
TI  - Degos Syndrome
A1  - Bissonnette, Bruno
A1  - Luginbuehl, Igor
A1  - Engelhardt, Thomas
Y1  - 2019
N1  - 
T2  - Syndromes: Rapid Recognition and Perioperative Implications, 2e
AB  - It  is  a  very  rare  form  of  systemic  occlusive  arteriopathy  involving  small-  and  medium-size  arteries  and  characterized  by  a  typical  two-stage  evolution.  The  disease  affects  vessels  of  the  dermis  causing  an  erythematous  aspect  with  dome-shaped  papules  that  develop  a  central  area  of  necrosis  and  leave  a  porcelain-like  scar.  Other  clinical  features  include  gastrointestinal  tract  and  central  nervous  system  involvement.  Other  organs  such  as  the  kidneys,  lungs,  pleura,  liver,  heart,  and  eyes,  can  also  be  involved.  The  gastrointestinal  form  of  Degos  disease  can  be  fatal.  The  onset  of  the  vascular  symptoms  happens  between  the  ages  of  15  and  50  years.  When  it  affects  teenagers,  especially  white  male,  the  initial  symptoms  are  skin  lesions  on  the  trunk.  
SN  - 
PB  - McGraw-Hill Education
CY  - New York, NY
Y2  - 2024/04/19
UR  - accessanesthesiology.mhmedical.com/content.aspx?aid=1164067646
ER  -