TY - CHAP M1 - Book, Section TI - Long-Chain 3-Hydroxyacyl-CoA Dehydrogenase Deficiency (LCHADD) A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas Y1 - 2019 N1 - T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - The mitochondrial trifunctional protein (MTP) is located on the inner mitochondrial membrane and catalyzes three of the four chain-shortening reactions in the mitochondrial β-oxidation of long-chain fatty acids. The three enzymes involved in these reactions are 2-enoyl coenzyme A (CoA) hydratase, long-chain 3-ketoacyl CoA thiolase, and long-chain 3-hydroxy acyl-coenzyme A dehydrogenase (LCHAD), which catalyzes the conversion of long-chain 3-hydroxyacyl-CoA esters into 3-ketoacyl-CoA esters. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164060644 ER -