TY - CHAP M1 - Book, Section TI - Uhl Anomaly A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Marciniak, Bruno A1 - Dalens, Bernard J. PY - 2006 T2 - Syndromes: Rapid Recognition and Perioperative Implications AB - A congenital disease characterized by the absence of a normal development of the myocardial layer of the right ventricle (usually replaced by fibrous or fatty tissue). Because the myocardial layer is dysplastic, the endocardium and epicardium are in apposition, which results in severe dilatation and early congestive cardiac failure. Chest radiography demonstrates marked cardiomegaly and right-sided chamber enlargement. Echocardiography and right-ventricle angiography demonstrate increased right heart volumes, severe diffuse hypokinesis, and tricuspid valve regurgitation. SN - PB - The McGraw-Hill Companies CY - New York, NY Y2 - 2024/03/29 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=58088841 ER -