TY - CHAP M1 - Book, Section TI - MURCS Association A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - MURCS is an acronym that stands for MÜllerian duct aplasia, Renal aplasia, Cervicothoracic Somite dysplasia. It is a very rare disorder that affects only females. Clinically, it is characterized by the absence of the uterus, cervix, and upper part of the vagina, kidney agenesia or ectopia, and malformations of the radial ray (phocomelia), ribs, and cervicothoracic spine. Most of affected patients have congenital heart defects. The urogenital abnormalities include Müllerian duct agenesis and unilateral renal hypoplasia. In some cases, neural tube defects, such as occipital encephalocele, can be present. Some affected females exhibit craniofacial malformations. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/03/29 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164079683 ER -