TY - CHAP M1 - Book, Section TI - Landouzy-Dejerine Dystrophy A1 - Bissonnette, Bruno A1 - Luginbuehl, Igor A1 - Engelhardt, Thomas PY - 2019 T2 - Syndromes: Rapid Recognition and Perioperative Implications, 2e AB - It is a genetically transmitted neuromuscular disease with a slow progression and characterized by weakness of facial, shoulder, and/or upper arm muscles. Nowadays it is more frequently called Facio-Scapulo-Humeral Muscular Dystrophy. It is characterized by muscle weakness and atrophy in the upper body. The presence of muscle atrophy in the hamstring and trunk muscles is more frequent than reported. The disease is clinically present before the age of 20 years. The onset may be as early as infancy or rarely later in adulthood. Life expectancy is not shortened. SN - PB - McGraw-Hill Education CY - New York, NY Y2 - 2024/10/04 UR - accessanesthesiology.mhmedical.com/content.aspx?aid=1164076276 ER -