Symptoms first appear in early childhood and
progress slowly throughout life with moderate disability. Beyond ataxia,
loss of reflexes, and muscular atrophy, clinical features can include
scoliosis, absent leg tendon jerks, distal sensory loss, static hand tremor,
abnormal gait, and slow peripheral nerve conduction velocity. Absence of
cerebellar signs, speech disturbances, Babinski sign, and nystagmus.