Acronym for lentigines (multiple),
electrocardiographic conduction abnormalities, ocular hypertelorism,
pulmonary stenosis, abnormal genitalia, retardation of growth, and deafness
(sensorineural). Complex congenital dysmorphogenetic disorder associating
mainly skin lesions (lentigines), severe cardiac anomalies (dysrhythmias,
pulmonary valve stenosis), ocular hypertelorism, abnormalities of genitalia,
sensorineural deafness, and severe retardation of growth.