Neuronal Ceroid Lipofuscinoses: Kufs Disease, also known as Juvenile Neuronal Ceroid Lipofuscinosis type IV,
is characterized by an onset in late adolescence or early adulthood. The clinical symptoms
include muscle weakness, ataxia, lack of muscle coordination, chorea, confusion, behavioral changes,
and seizures. Batten Disease, also known as type III juvenile form
of Neuronal Ceroid Lipofuscinosis, is characterized by an onset
during childhood or early adolescence and most often presenting clinical
features of rapid visual loss, deterioration of earlier psychomotor development,
behavior changes, and severe seizure activities. Individuals affected with this condition
often develop kyphoscoliosis. It is inherited as an autosomal recessive
trait.