Characteristic skin lesions that vary
considerably in their expression: vesiculopustular lesions on the hands and
feet that resolve by late childhood; widespread eczematoid dermatitis that
resolves by age 5 years; diffuse poikiloderma with striate and reticulate
atrophy that develops gradually, but spares the face, scalp, and ears, and
persists into adulthood; keratotic papules on the hands, feet, elbows, and
knees that appear before the age of 5 years and persist indefinitely; traumatic
bullae at pressure sites that heal with atrophic scars. Patients
are extremely photosensitive.