Enlarging hemangioma-like lesion, mainly
cutaneous (especially on the extremities) but also visceral. DIC (decreased
platelets and fibrinogen, presence of increased d-dimers). Often
inoperable. Treatment options: vincristine, interferon-α, steroids,
ticlopidine with aspirin, or radiotherapy. Untreated Kasabach-Merritt
syndrome has a 10 to 37% mortality rate.