Sections View Full Chapter Figures Tables Videos Annotate Full Chapter Figures Tables Videos Supplementary Content + At a Glance Download Section PDF Listen ++ Polymalformative syndrome characterized by dental malformations and various distal skeletal anomalies. + Synonyms Download Section PDF Listen ++ Mesomelic Dysplasia, Thai Type; Mesomelic Dysplasia with Ankle, Carpal, and Tarsal Synostosis; Mesomelic Dysplasia, Kantaputra Type; Molarization of Anterior Teeth with Deafness. + Incidence and Genetic Inheritance Download Section PDF Listen ++ Incidence and mode of inheritance are unknown. Only one case report of an affected female. + Clinical Aspects Download Section PDF Listen ++ Molarization and premolarization of anterior teeth, possibly as a consequence of a mesenchymal defect. Histologically, tooth structure was normal; sensorineural deafness; flared nares. + Anesthetic Considerations Download Section PDF Listen ++ Careful laryngoscopy is recommended to avoid dental injuries. + References Download Section PDF Listen ++Kantaputra PN, Gorlin RJ: Double dens invaginatus of molarized maxillary central incisors, premolarization of maxillary lateral incisors, multituberculism of the mandibular incisors, canines and first premolar, and sensorineural hearing loss. Clin Dysmorphol 1:128, 1992. [PubMed: 1285271]