Dysplastic malformation of the anterior segment
of the eye characterized by the combination of congenital cataract and
microcornea (diameter <11 mm). Occasionally, other ocular anomalies such as
iris coloboma, sclerocornea, myopia, or Peters anomaly (central corneal
opacity associated with abnormal corneal development that may result in
cataract, adhesions of the iris to the cornea, and glaucoma) may be present.