Common features are pain (38%), ureteral
colics (28%), polyuria (28%), urinary tract infections, or hematuria.
Often it is an incidental finding during evaluation of the abdomen or the
urinary tract for other reasons. In the absence of complications, the
overall renal function is and remains normal. Other features can include
hypercalciuria (common), hyperuricosuria, urolithiasis, acidification of the
urine, or impairment of urinary concentration. If renal involvement is
segmental, surgical resection may be beneficial. A higher incidence of Wilms
tumor and other abdominal malignancies has been reported in patients
diagnosed with CRS during childhood. Regular followup in this population is
mandatory.