Sections View Full Chapter Figures Tables Videos Annotate Full Chapter Figures Tables Videos Supplementary Content + At a Glance Download Section PDF Listen ++ Genetic syndrome characterized by multiple osseous dysplasia, ear anomalies, and short stature. + Synonym Download Section PDF Listen ++ Auriculo-Osteodysplasia. Do not confuse with congenital contractural arachnodactyly, which sometimes is also referred to as Beals syndrome. + Incidence and Genetic Inheritance Download Section PDF Listen ++ Two families with autosomal dominant inheritance have been reported. Ratio of females to males is approximately 1:1. The genetic defect has not been identified. + Clinical Aspects Download Section PDF Listen ++ Dysplasia of the radiocapitellar joint with or without dislocation of the radial head, characteristically shaped ears with elongated and attached earlobes, and an associated small lobule beneath are the hallmarks of this syndrome. Hip dislocation is more frequent in these families. Females tend to have masculine torsos. All affected individuals have a slightly reduced body height. Intelligence is normal. + Anesthetic Considerations Download Section PDF Listen ++ Based on the described features, no specific implications for anesthesia are expected. However, positioning the patient requires care to prevent luxation of the affected joints, especially with use of neuromuscular blocking agents. + References Download Section PDF Listen ++Beals RK: Auriculo-osteodysplasia: A syndrome of multiple osseous dysplasia, ear anomaly, and short stature. J Bone Joint Surg Am 49A:1541, 1967.